Gastroschisis
Gastroschisis Ventral body wall defect resulting from a lack of closure of the lateral body wall folds in the abdominal region resulting in protrusion of intestines and sometimes other organs through the defect.
It occurs lateral to the umbilicus usually on the right
Cause : abnormal closure of body wall around the connecting stalk
Content: intestines, other organs including the stomach and liver protruded, which are not covered by peritoneum or amnion
Out come : the bowel may be damaged by exposure to amniotic fluid
Diagnosis : like omphalocele it can be diagnosed later part of pregnancy by ultrasound
Incidence : 1/10000 birth but is increasing in frequency especially among young women <20 years old.
It is not associate with chromosomal abnormality or other birth defect like omphalocele so the survival rate is excellent
Death usually occurs due to volvulus formation (rotation of bowel ) resulting in compromised blood supply may kill large regions of the intestine and lead to fetal death .
No comments:
Post a Comment